(CF) is a genetic condition that affects the body's epithelial cells. These cells
are found in many places, including the sweat glands, lungs, and pancreas.
An error in the cells causes problems with the body's balance of salt and water.
The body responds by making thick mucus, which blocks the lungs
and sometimes other ducts and passageways, causing infections and breathing problems.
How Does Cystic Fibrosis Affect Nutrition?
The sticky mucus from cystic fibrosis can block normal absorption of key nutrients
and fat in the intestines, causing:
trouble gaining weight
greasy bowel movements
Why Do Some Teens Need Enzymes?
CF often causes a condition called pancreatic insufficiency. This
means the enzymes made in the pancreas that digest fat, carbohydrates, and protein
don't pass into the intestines
as they should. So the body can't digest food normally.
Teens with pancreatic insufficiency might have problems with growth and weight
gain. They also might have frequent and bad-smelling bowel movements. They'll need
to take prescribed enzymes with meals and snacks to help them digest food and keep
a healthy weight. A CF doctor will work with a dietitian to prescribe enzymes based
on weight, growth, and bathroom habits.
If you take pancreatic enzymes in pill form:
Enzymes should be taken with all foods and drinks that have fat and protein.
Enzymes should never be chewed or crushed. They must be swallowed whole.
Enzymes are sensitive to temperature. Store in a cool, dry place. Avoid extremes
in temperature, such as leaving enzymes in the car during the summer or winter months.
Consider taking an extra enzyme cap for large meals or fast food meals that are
What's a Healthy Diet for Someone With CF?
In the past, a healthy diet for someone with cystic fibrosis was high-calorie,
high-fat, and high-salt. But new therapies make weight gain easier and life expectancy
longer. So the focus of a healthy diet is changing. It's becoming more important to
consider how diet can keep you feeling healthy as you grow older. Healthy diet choices
can help prevent other conditions, such as heart disease or cancer, while improving
your quality of life.
Avoid sugary drinks like juice, soda, sweet tea, lemonade, etc.
Eat more homemade meals and less fast food or restaurant meals.
What's a Healthy Weight for Someone With CF?
A healthy weight for teens with cystic fibrosis is different for each person. Your
CF team will talk a lot about body
mass index (BMI). BMI is a way to measure if you are at a healthy weight (not
underweight or overweight) by comparing your weight to your height. The goal for all
teens with CF is to reach a healthy weight that supports healthy lungs. Talk to your
CF doctor or dietitian if you have questions about your healthy weight goals.
Salt. Teens with CF lose more salt in their sweat than their peers.
The dietitian may suggest adding extra salt to foods, eating salty snacks, and drinking
sports drinks when teens exercise or spend time outdoors in hot weather.
Fat-soluble vitamins (vitamins A, D, E, and K). These vitamins
are important for immune function, growth, and healing. They're absorbed along with
fat. Most teens with CF have trouble digesting and absorbing fat, which means they
may not absorb fat-soluble vitamins.
Your fat-soluble vitamin levels will be checked once a year, and you might take a
prescription CF-specific multivitamin.
Calcium. Teens with CF, especially those with pancreatic insufficiency,
are at risk for osteopenia or osteoporosis (weak, brittle bones).
Dairy products are good sources of calcium
(and the full-fat varieties also are good sources of fat and calories). If you don't
drink cow's milk, consider trying a milk alternative that is fortified with calcium.
Calories. Some teens with CF need extra calories to grow healthy
and strong. The extra calories should come from a well-balanced, healthy diet.
How Can Teens Reach High-Calorie Needs?
Some teens with CF need more calories than their peers. The best way to meet these
calorie needs is by eating a well-balanced diet, but adding extra calories with added
fat. Here are some tricks for adding extra calories to your day:
Add extra butter or oil to pasta, rice, potatoes, or cooked vegetables.
Pair raw vegetables with salad dressing or hummus.
Top salads and sandwiches with avocados or guacamole.
Grill sandwiches in butter or margarine.
Add a splash of heavy cream to milk, oatmeal, smoothies, or cream-based soups.
Focus on high-calorie snacks. Try trail mix, peanut butter and banana sandwiches,
full-fat yogurt with granola, or cheese crackers.
Why Do Some Teens Need Nutrition Supplements or Tube Feedings?
Some teens with CF may have trouble gaining weight from a high-calorie diet alone.
A doctor or dietitian may recommend adding nutrition supplements to your diet. Nutrition
supplements are calorie-rich drinks that also have protein, vitamins, and minerals.
For some teens, this added source of calories is enough to improve weight gain.
If a high-calorie diet and nutrition supplements are not enough, a doctor or dietitian
may recommend tube feedings. These feedings, done through a tube into the stomach,
are often given at night for extra calories. These overnight feedings leave teens
with CF free to enjoy normal meals and activities during the day.
Making the decision to get a feeding tube can be hard, but many teens and families
express relief afterward. Tube feedings can help teens gain weight, while easing the
stress and conflict around food and eating. Having a tube put in for the feedings
usually is a simple procedure that doesn't need extensive surgery or a long hospital
What Else Should I Know?
Meeting the unique nutrition needs of CF isn't always easy. Work with your team
to set nutrition goals that you can reach. If talking about food or nutrition feels
stressful, consider working with the psychologist on your CF team. They can help you
manage the emotions linked to how you eat.
Besides the right diet, exercise can help support better lung health, mood, and
quality of life. Talk to your doctor or the physical
therapist on your CF team about the right kind of exercise for you.