Lennox-Gastaut Syndromeenparentshttps://kidshealth.org/EN/images/headers/Lennox-Gastaut_Syndrome_enHD_1.jpgLennox-Gastaut syndrome (LGS) is a seizure disorder. Children with LGS have several different kinds of seizures.Lennox-Gastaut syndrome, LGS, Atypical absence seizures, automatisms, myoclonic seizures, Tonic-clonic seizures, brain injury, seizure disorder, seizures, epilepsy, epileptic, Tonic seizures, atonic, tonic, PET/MRI, siezures, central nervous system, seesures, seezures, seeshures, sesures, generalized seizures, partial seizures, brain, brains, brain problems, fits, shaking, postictal phase, ketogenic diet, ketogenic, electrical signals, vagal nerve stimulators, vagal, breakthrough seizures, neurologists, neurology, CD1Neurosurgery, CD1Epilepsy, CD1Neurology08/22/201711/03/201709/02/2019Harry T. Chugani, MD10/17/2017f8ee7add-7856-4bc1-ab1a-33a0acd90bd3https://kidshealth.org/ws/RadyChildrens/en/parents/lennox-gastaut-syndrome.html/<h3>What Is Lennox-Gastaut Syndrome?</h3> <p>Lennox-Gastaut syndrome (LGS) is a <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/seizure.html/">seizure</a> disorder. Children with LGS will have:</p> <ol> <li>several different kinds of seizures</li> <li>some degree of intellectual disability</li> <li>abnormal findings on an <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/eeg.html/">EEG</a>&nbsp;(a test to see brain waves/electrical activity)</li> </ol> <p>LGS begins in children when they're 3 to 5 years old. It's a lifelong condition that requires a high level of care.</p> <h3>What Kinds of Seizures Happen in Lennox-Gastaut Syndrome?</h3> <p>The different seizure types in LGS can cause a variety of symptoms.</p> <h5>Seizure Types</h5> <p><strong>Tonic seizures:</strong></p> <ul> <li>muscles suddenly become stiff</li> <li>last about 20 seconds</li> <li>usually involve both sides of the body</li> <li>often happen during sleep</li> </ul> <p><strong>Atonic seizures:</strong></p> <ul> <li>muscles briefly and unexpectedly go weak or limp (called "drop attacks")</li> <li>last less than 20 seconds</li> <li>can involve the whole body or just certain parts</li> <li>after the seizure, the child recovers quickly</li> </ul> <p><strong>Other types:</strong></p> <ul> <li><strong>Atypical absence seizures:</strong> staring spells with blinking, smacking or chewing, rubbing hands together (called <strong>automatisms</strong>)</li> <li><strong>Myoclonic seizures:</strong> brief muscle twitches or jerks in the neck, shoulders, upper arms, and face</li> <li><strong>Tonic-clonic seizures:</strong> convulsions with rhythmic jerks, rigid muscles, loss of consciousness, and eyes rolling back</li> </ul> <h3>What Causes Lennox-Gastaut Syndrome?</h3> <p>Lennox-Gastaut syndrome can be caused by multiple conditions. For example, early brain injury from infection or trauma, genetic causes, or brain malformations can all lead to LGS.</p> <p>Sometimes, LGS has no clear cause.</p> <h3>How Is Lennox-Gastaut Syndrome Diagnosed?</h3> <p>LGS is diagnosed by a pediatric neurologist (a doctor who specializes in brain, spine, and nervous system problems). Testing includes:</p> <ul> <li><a href="https://kidshealth.org/ws/RadyChildrens/en/parents/eeg.html/">EEG</a>. Children with LGS will have a pattern showing "generalized slow spike and wave."</li> <li>VEEG, or video electroencephalography (EEG with video recording)</li> <li><a href="https://kidshealth.org/ws/RadyChildrens/en/parents/ct-head.html/">CAT scan</a> and <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/mri-brain.html/">MRI</a> to look inside the brain</li> </ul> <h3>How Is Lennox-Gastaut Syndrome Treated?</h3> <p>Seizures in LGS don't usually respond well to medicines. Other treatments include:</p> <ul> <li>neurostimulation (a device that stimulates nerves to stop seizures)</li> <li>the <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/ketogenic-diet.html/">ketogenic diet</a> (a strict high-fat, low-carbohydrate diet)</li> <li><a href="https://kidshealth.org/ws/RadyChildrens/en/parents/epilepsy-surgery.html/">surgery</a>, such as corpus callosotomy where the "bridge" that connects the two brain hemispheres is cut. This works best for tonic and atonic seizures, and might not help the other types of seizures.</li> </ul> <h3>How Can I Help My Child?</h3> <p>Caring for a child with LGS can be challenging. Work with your child's care team to set up needed appointments and therapies.</p> <p>Make sure that you and other adults and caregivers (family members, babysitters, teachers, coaches, etc.) know <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/seizures-sheet.html/">what to do</a> during a seizure. Your child may need to wear a helmet to prevent head injury during seizures.</p>Síndrome de Lennox-GastautEl síndrome de Lennox-Gastaut es un trastorno convulsivo. Los niños con este síndrome tienen varios tipos distintos de convulsiones https://kidshealth.org/ws/RadyChildrens/es/parents/lennox-gastaut-syndrome-esp.html/8758b21c-3378-45c5-8aee-6c0690ff45ce
Benign Rolandic EpilepsyKids with benign rolandic epilepsy of childhood (BREC) have seizures that involve twitching, numbness, or tingling of the face or tongue.https://kidshealth.org/ws/RadyChildrens/en/parents/brec.html/cacf42b8-6bd0-4265-92db-97852a24d2cd
Childhood Absence Epilepsy (CAE)Kids with childhood absence epilepsy (CAE) have seizures where they "blank out" for a few seconds. Most kids will outgrow CAE.https://kidshealth.org/ws/RadyChildrens/en/parents/childhood-absence-epilepsy.html/612e939f-cd06-4a14-8904-279264e58bb8
EpilepsySeizures are a common symptom of epilepsy, a condition that affects millions of people worldwide. Learn all about epilepsy, including what to do if you see someone having a seizure.https://kidshealth.org/ws/RadyChildrens/en/teens/epilepsy.html/85df049a-dc59-41a5-b92c-421ea2d711be
Epilepsy Factsheet (for Schools)What teachers should know about epilepsy, and what they can do to help students with the condition succeed in school.https://kidshealth.org/ws/RadyChildrens/en/parents/epilepsy-factsheet.html/83a2f877-3f5b-41d4-949f-1e24584cfabc
Epilepsy SurgeryEpilepsy surgery is an operation done on the brain to reduce or stop seizures.https://kidshealth.org/ws/RadyChildrens/en/parents/epilepsy-surgery.html/62a50c44-d6c5-44e2-b4d2-697d4d8aa46c
First Aid: Febrile SeizuresFebrile seizures are convulsions that happen in some children with fevers. They usually stop on their own after a few minutes and don't cause any other health problems.https://kidshealth.org/ws/RadyChildrens/en/parents/febrile-seizures-sheet.html/804b66fe-076e-4851-9990-ef93e771fe1d
Intractable EpilepsyIntractable epilepsy is when a child's seizures can't be controlled by medicines. Doctors may recommend surgery or other treatments for intractable seizures.https://kidshealth.org/ws/RadyChildrens/en/parents/intractable-epilepsy.html/b8735f52-1cd8-4dc4-9c1e-b0af479bdac5
Juvenile Myoclonic EpilepsyKids with juvenile myoclonic epilepsy (JME) have one or more of several different kinds of seizures, which begin around the age of puberty.https://kidshealth.org/ws/RadyChildrens/en/parents/juvenile-myoclonic-epilepsy.html/f594267f-fabd-48e1-95b8-45e3483b107a
Ketogenic DietA ketogenic diet is a strict high-fat, low-carbohydrate diet that can reduce, and sometimes stop, seizures.https://kidshealth.org/ws/RadyChildrens/en/parents/ketogenic-diet.html/fcd721e8-9e89-4044-96ae-730331fd0bc3
PET/MRI ScanA PET/MRI scan is an imaging test that combines PET and MRI in one session. It creates very detailed pictures of the inside of the body. https://kidshealth.org/ws/RadyChildrens/en/parents/pet-mri.html/bb266abc-6708-495f-8b79-8b21b1477b5e
SeizuresSeizures are caused by a sudden surge of electrical activity in the brain. Find out what you need to know about seizures and what to do if your child has one.https://kidshealth.org/ws/RadyChildrens/en/parents/seizure.html/17184860-dea1-4cd4-95ba-3cf34539cd44
Temporal Lobe EpilepsyKids with temporal lobe epilepsy (TLE) have seizures that start in one of the temporal lobes of the brain. Seizures usually get better with medicine.https://kidshealth.org/ws/RadyChildrens/en/parents/temporal-lobe-epilepsy.html/a45446cb-f4f8-4aa6-a259-9248db76f764
kh:age-allAgesOrAgeAgnostickh:clinicalDesignation-neurologykh:genre-articlekh:primaryClinicalDesignation-neurologyBrain & Nervous Systemhttps://kidshealth.org/ws/RadyChildrens/en/parents/medical/brain/d6b00a11-9db0-403c-bc41-00bcdf022537