A to Z: Hypoplastic Left Heart Syndromeenparentshttps://kidshealth.org/EN/images/headers/P-khAZDictionary-enHD-AR1.jpgLearn about hypoplastic left heart syndrome, a rare and serious defect of the heart.hypoplastic left heart syndrome, HLHS, congenital heart defect, cyanosis, cold extremities, weak pulse, lethargy, poor feeding, heart transplant, Norwood operation, bi-directional Glenn procedure, Fontan procedure, heart, heart defects, birth defects, CD1 Cardiology, CD1Hypoplastic Left Heart Syndrome, CD1Congenital Heart Defects02/18/201303/18/201909/02/2019d6c38a86-a89f-428b-8c85-097dc9da1a70https://kidshealth.org/ws/RadyChildrens/en/parents/az-hypoplastic.html/<p><em>May also be called: HLHS</em></p> <p>Hypoplastic (HI-puh-plas-tik) left heart syndrome (HLHS) is a rare and serious defect in which the structures of the left side of the <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/heart.html/">heart</a> (the left ventricle, the mitral valve, and the aortic valve) are underdeveloped. As a result, <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/blood.html/">blood</a> cannot be adequately pumped throughout the body.</p> <h3>More to Know</h3> <p>Hypoplastic left heart syndrome is present at birth (<a class="kh_anchor">congenital</a>) and has no known cause. It is usually diagnosed within the first few days of life. Without surgery to repair the heart, HLHS is fatal.</p> <p>Symptoms of HLHS include blue or gray skin color (cyanosis), rapid breathing, pounding heart, shortness of breath, cold hands and feet, weak pulse, unusual drowsiness and poor feeding.</p> <p>Once diagnosed with HLHS, most babies will undergo a series of three operations beginning shortly after birth and ending at 3 years of age. For some babies, <a href="https://kidshealth.org/ws/RadyChildrens/en/parents/heart-transplant.html/">heart transplant</a> is the best option if a donated organ is available.</p> <h3>Keep in Mind</h3> <p>While many babies now survive HLHS, they need to be monitored closely by a cardiologist for the rest of their lives. Many complications can occur with HLHS and sometimes additional heart surgery or even heart transplant may be necessary as children born with HLHS get older.</p> <p><em>All A to Z dictionary entries are regularly reviewed by KidsHealth medical experts.</em></p>
Atrial Septal Defect (ASD)Atrial septal defect (ASD) — also known as a "hole in the heart" — is a type of congenital heart defect. Most ASDs are diagnosed and treated successfully.https://kidshealth.org/ws/RadyChildrens/en/parents/asd.html/2853e7be-1368-420f-bc8d-134350949604
Coarctation of the AortaCoarctation of the aorta (COA) is a narrowing of the aorta, the major blood vessel that carries blood away from the heart to the body.https://kidshealth.org/ws/RadyChildrens/en/parents/coa.html/c608c070-bf56-4f7e-97ed-025cfc1ca1a6
Congenital Heart DefectsHeart defects happen when there's a problem with a baby's heart development during pregnancy. Most heart defects can be treated during infancy.https://kidshealth.org/ws/RadyChildrens/en/parents/if-heart-defect.html/3dd23fa7-906f-4df9-8638-7400b77bed42
Heart and Circulatory SystemThe heart and circulatory system are our body's lifeline, delivering blood to the body's tissues. Brush up on your ticker with this body basics article.https://kidshealth.org/ws/RadyChildrens/en/parents/heart.html/52398b6a-54a6-4272-a569-42ed5b12aeac
Patent Ductus Arteriosus (PDA)The ductus arteriosus is a blood vessel that connects two major arteries before birth and normally closes after a baby is born. If it stays open, the result is a condition called patent ductus arteriosus (PDA).https://kidshealth.org/ws/RadyChildrens/en/parents/patent-ductus-arteriosus.html/1220a363-ed10-4541-94c6-ecb923902cd8
Ventricular Septal Defect (VSD)Ventricular septal defect (VSD) — also known as a "hole in the heart" — is a congenital heart defect. Most VSDs are diagnosed and treated successfully.https://kidshealth.org/ws/RadyChildrens/en/parents/vsd.html/21135699-6b44-43bd-96b1-618186631849
When Your Baby Has a Birth DefectIf your child has a birth defect, you don't have to go it alone - many people and resources are available to help you.https://kidshealth.org/ws/RadyChildrens/en/parents/baby-has-birth-defect.html/9c0573a4-68a2-4d7d-a868-26999e332361
When Your Child Needs a Heart TransplantIf your child needs a heart transplant, you're probably feeling lots of emotions. Fortunately, many kids who undergo heart transplants go on to live normal, healthy lives.https://kidshealth.org/ws/RadyChildrens/en/parents/heart-transplant.html/0c94f853-a992-413c-b67f-2ed97ac42ec6
kh:age-allAgesOrAgeAgnostickh:clinicalDesignation-cardiologykh:genre-dictionarykh:primaryClinicalDesignation-cardiologyHhttps://kidshealth.org/ws/RadyChildrens/en/parents/dictionary/h/c2d4f543-6c0d-4809-85ed-87a4ce512e91Cardiology A to Zhttps://kidshealth.org/ws/RadyChildrens/en/parents/dictionary/az-cardio/04be85fa-f4f5-44c2-a321-21821f326c6a